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Braz J Cardiovasc Surg. 2019 Jun 1;34(3):372-376. doi: 10.21470/1678-9741-2018-0114.

Rapidly Progressive Malignant Fibrous Histiocytoma of Right Atrium: a Rare Case Report.

Author information

1
Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital Department of Cardiovascular Surgery İstanbul Turkey Department of Cardiovascular Surgery, Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey.
2
Kanuni Sultan Suleyman Training and Research Hospital Department of Pathology İstanbul Turkey Department of Pathology, Kanuni Sultan Suleyman Training and Research Hospital, İstanbul, Turkey.

Abstract

We are going to present a case of malignant fibrous histiocytoma in the right atrium, which is a very rare entity. The patient had a right atrial mass, which prolapsed through the tricuspid valve into the right ventricle, causing functional tricuspid valve stenosis. The tumor was completely resected and the patient had an uneventful postoperative period. Histopathological examination reported malignant fibrous histiocytoma. The patient presented to the emergency department five weeks after discharge with dyspnea and palpitation. Echocardiography and magnetic resonance imaging revealed recurrent right atrial tumor mass. His clinical status has worsened, with syncope and acute renal failure. On the repeated echocardiography, suspected tumor recurrence was observed in left atrium, which probably caused systemic embolization. Considering the aggressive nature of the tumor and systemic involvement, our Heart Council decided to provide palliative treatment by nonsurgical management. His status deteriorated for the next few days and the patient succumbed to a cardiac arrest on the 4th day.

KEYWORDS:

Malignant Fibrous Histiocytoma; Right Atrium; Undifferentiated Pleomorphic Sarcoma

PMID:
31310479
PMCID:
PMC6629222
DOI:
10.21470/1678-9741-2018-0114
[Indexed for MEDLINE]
Free PMC Article

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