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Ann Maxillofac Surg. 2019 Jan-Jun;9(1):208-210. doi: 10.4103/ams.ams_281_18.

Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up.

Author information

1
Department of Oral and Maxillofacial Surgery, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India.
2
Department of Paediatric Dentistry, Kanchi Kamakoti Childs Trust Hospital, Chennai, Tamil Nadu, India.
3
Department of Paediatric Anaesthesiology, Kanchi Kamakoti Childs Trust Hospital, Chennai, Tamil Nadu, India.

Abstract

Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment involves surgical resection as primary modality. Prognosis is much better compared to the adult variant with even scope for spontaneous regression following "conservative" resection. We present a case of IFS of the nasomaxillary complex in a 3-month-old female child. We managed our case with surgical resection, and the patient has remained disease free for over 2 years.

KEYWORDS:

Fibroblastic tumor; hemangioma; infantile fibrosarcoma; teratoma

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