Pediatric Tracheal Rhabdomyosarcoma Masquerading as a Granuloma

Marcus Hershey; Casie M James; Maria Velez; Jhanvi Kanotra; Randall Craver; Sohit Paul Kanotra

doi:10.4103/jiaps.JIAPS_107_18

Pediatric Tracheal Rhabdomyosarcoma Masquerading as a Granuloma

J Indian Assoc Pediatr Surg. 2019 Jul-Sep;24(3):212-215. doi: 10.4103/jiaps.JIAPS_107_18.

Authors

Marcus Hershey¹, Casie M James¹, Maria Velez², Jhanvi Kanotra³, Randall Craver⁴, Sohit Paul Kanotra^{1

5}

Affiliations

¹ Department of Otolaryngology-Head and Neck Surgery, Louisiana State University, Louisiana, USA.
² Section of Hematology and Oncology, Children's Hospital New Orleans, Louisiana State University, Louisiana, USA.
³ Department of Pathology, Louisiana State University, Louisiana, USA.
⁴ Department of Pathology and Pediatrics, Children's Hospital New Orleans, Louisiana State University Health Science Center, Louisiana, USA.
⁵ Department of Pediatric Otolaryngology, Children's Hospital New Orleans, Louisiana, USA.

Abstract

We describe a posterior wall intratracheal embryonal rhabdomyosarcoma (RMS) arising in a 6-year-old tracheostomized child masquerading as reactive granulation tissue and review all reported cases of pediatric intratracheal RMS. The child underwent laser debulking of the tumor and postoperative radiation and chemotherapy with no evidence of recurrence at 2-year follow-up. A literature review revealed four previous cases of pediatric primary tracheal or intratracheal RMS, and remission was achieved in all but one case with surgery, chemotherapy, and radiation. Pathologic evaluation of tracheal mucosal granulation tissue may merit consideration, particularly in patients with increased risk factors.

Keywords: Granuloma; pediatric; rhabdomyosarcoma; trachea; tracheostomy.

Publication types

Case Reports