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Indian J Ophthalmol. 2019 Jul;67(7):1240-1245. doi: 10.4103/ijo.IJO_1553_18.

Solitary orbital myofibroma in a child: A rare case report with literature review.

Author information

1
Ophthalmic Plastic Surgery, Orbit and Ocular Oncology Services, The Operation Eyesight Universal Institute for Eye Cancer, Bhubaneswar, Odisha, India.
2
Kanupriya Dalmia Ophthalmic Pathology Laboratory, L.V. Prasad Eye Institute, Mithu Tulsi Chanrai Campus, Bhubaneswar, Odisha, India.

Abstract

Myofibroma is a rare benign mesenchymal tumor of uncertain histogenesis. A six-year-old boy presented with a unilateral lower eyelid mass of six weeks' duration. MRI revealed a circumscribed mass in the inferolateral orbit with bony erosion. A systemic examination was unremarkable. Excision with histopathology revealed a partially infiltrative spindle cell tumor with bland nuclear morphology expressing smooth muscle actin and muscle-specific actin, compatible with myofibroma. Solitary myofibroma is a rare childhood orbital tumor and may clinico-radiologically closely mimic a malignancy. Histopathology and immunohistochemistry can help reach a definitive diagnosis. Systemic evaluation and close follow up are crucial in such cases.

KEYWORDS:

Benign; bone erosion; children; myofibromatosis; orbital myofibroma

PMID:
31238482
DOI:
10.4103/ijo.IJO_1553_18
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