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J Cancer Res Ther. 2019 Jul-Sep;15(3):729-732. doi: 10.4103/jcrt.JCRT_939_16.

Hemangiopericytoma of supraglottis: A rare case report and review of literature.

Author information

1
Department of Medical and Paediatric Oncology, Gujarat and Cancer Research Institute, Ahmedabad, Gujarat, India.
2
Department of Radiology, Gujarat and Cancer Research Institute, Ahmedabad, Gujarat, India.
3
Department of Pathology, Gujarat and Cancer Research Institute, Ahmedabad, Gujarat, India.

Abstract

In 1942, Stout and Murray first used the term hemangiopericytoma to describe a tumor which is distinguished histologically from other types of vascular neoplasm characterized by proliferation of pericytes. It is a rare neoplasm that was originally described as a vascular tumor derived from the pericytes. They account for 2%-3% of all soft tissue sarcomas in humans and they occur mainly in the musculoskeletal system. About 15%-30% of all hemangiopericytomas occur in the head and neck region. Hemangiopericytoma of supraglottis is very rare neoplasm with only nine cases reported in literature and ours is the tenth case overall and first case in pediatric age group. Herein, we are presenting an extremely rare case report of hemangiopericytoma of supraglottis in a 6-year-old male child who presented with stridor followed by which tracheostomy was done. Later, the patient was treated initially with radiotherapy followed by surgery, i.e., laryngectomy in view of residual disease postcurative radiotherapy. Hence, hemangiopericytoma is a very rare tumor overall and can present in pediatric age group and can be one most important differential diagnosis because many patients in this age group, stridor most commonly occurs due to the infectious causes such as influenza virus and diphtheria-induced croup, i.e., laryngotracheobronchitis.

KEYWORDS:

Hemangiopericytoma; radiotherapy; supraglottis

PMID:
31169253
DOI:
10.4103/jcrt.JCRT_939_16
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