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Echocardiography. 2018 Oct;35(10):1684-1691. doi: 10.1111/echo.14124. Epub 2018 Aug 23.

Multimodality imaging of scimitar syndrome in adults: A report of four cases.

Author information

1
The Leon H Charney Division of Cardiology, New York University Langone Health, New York City, New York.
2
Department of Radiology, New York University Langone Health, New York City, New York.
3
Department of Pediatrics, New York University Langone Health, New York City, New York.
4
Department of Medicine (Cardiology), VA New York Harbor Health Care System (Manhattan Campus), New York City, New York.

Abstract

Partial anomalous pulmonary venous return (PAPVR) comprises a group of congenital cardiovascular anomalies associated with pulmonary venous flow directly or indirectly into the right atrium. Scimitar syndrome is a variant of PAPVR in which the right lung is drained by right pulmonary veins connected anomalously to the inferior vena cava. Surgery is the definitive treatment for scimitar syndrome. However, it is not always necessary as many patients are asymptomatic, have small left-to-right shunts, and enjoy a normal life expectancy without surgery. We report multimodality imaging in four adults with scimitar syndrome and the implications for management of this rare syndrome.

KEYWORDS:

cardiac magnetic resonance imaging; congenital cardiac anomalies; partial anomalous pulmonary venous return; scimitar syndrome; transesophageal echocardiogram; transthoracic echocardiogram

PMID:
30136740
DOI:
10.1111/echo.14124
[Indexed for MEDLINE]

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