Format

Send to

Choose Destination
Rev Port Cardiol. 2018 Apr;37(4):341-350. doi: 10.1016/j.repc.2017.09.015. Epub 2018 Feb 26.

Congenital anomalies of the coronary arteries.

[Article in English, Portuguese]

Author information

1
Faculdade de Medicina da Universidade do Porto, Portugal. Electronic address: andrea_aeps@hotmail.com.
2
Serviço da Cardiologia Pediátrica, Centro Hospital São João, Porto, Portugal; Departamento de Pediatria, Faculdade de Medicina da Universidade do Porto, Porto, Portugal.
3
Serviço de Medicina Interna, Centro Hospitalar São João, Porto, Portugal.

Abstract

Congenital coronary artery anomalies are modifications of their origin, course or structure and its incidence varies between 0,2 and 5,6% of the general population. Although the majority is asymptomatic, they are the second leading cause of sudden cardiac death in young athletes. The aim of this study is to highlight the main anomalies with hemodynamic significance, including the anomalous origin of a coronary artery from the opposite sinus and anomalous origin of the left coronary artery from pulmonary artery. The anomalous aortic origin of a coronary artery from the opposite sinus accounts for 14-16% of all cardiac deaths, that unexpectedly occur in healthy children or young athletes during or immediately after exercise. The mechanism responsible for the compression/occlusion of the coronary artery originating from the opposite sinus is still unclear and there are several proposed mechanisms. The clinical presentation of these patients is variable and physical examination is normal in most individuals. Transthoracic echocardiogram is the diagnostic test most commonly used. Treatment and management are controversial topic. The anomalous origin of the left coronary artery from pulmonary artery is a very rare condition and without surgery, most infants die within the first 12 months of life. The echocardiogram is also the method of choice for diagnostic confirmation. The diagnosis of this congenital anomaly in an infant, usually seriously ill, is an indication for urgent surgery. Because these anomalies produce hemodynamic changes, it is important an early diagnosis and treatment.

KEYWORDS:

Anomalias da origem das artérias coronárias na aorta; Anomalias da origem das artérias coronárias na artéria pulmonar; Anomalias das artérias coronárias; Anomalous aortic origin of the coronary artery; Anomalous origin of the coronary artery from pulmonary artery; Cardiac sudden death; Coronary vessel anomalies; Morte súbita de origem cardíaca

PMID:
29496389
DOI:
10.1016/j.repc.2017.09.015
[Indexed for MEDLINE]
Free full text

Supplemental Content

Full text links

Icon for Elsevier Science
Loading ...
Support Center