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Retina. 2018 Jan;38 Suppl 1:S67-S78. doi: 10.1097/IAE.0000000000001836.

CONCURRENT IDIOPATHIC MACULAR TELANGIECTASIA TYPE 2 AND CENTRAL SEROUS CHORIORETINOPATHY.

Author information

1
Department of Ophthalmology, University of Lausanne, Jules-Gonin Eye Hospital, Fondation Asile des Aveugles, Lausanne, Switzerland.
2
Rotterdam Eye Hospital, Rotterdam, the Netherlands.
3
Division of Epidemiology and Clinical Applications, National Eye Institute, National Institutes of Health, Bethesda, Maryland.
4
INSERM, U1138, Team 17, Physiopathology of Ocular Diseases to Clinical Development, Université Paris Descartes Sorbonne Paris Cité, Centre de Recherche des Cordeliers, Paris, France.
5
Faculty of Biology and Medicine, University of Lausanne, Lausanne, Switzerland.
6
Vitreous, Retina, Macula Consultants of New York, New York, New York.
7
The LuEster T. Mertz Retina Research Laboratory, New York University, New York, New York.

Abstract

PURPOSE:

To describe cases presenting with features of idiopathic macular telangiectasia (MacTel) Type 2 and central serous chorioretinopathy (CSC).

METHODS:

Databases from four tertiary retina centers were searched for cases copresenting CSC and MacTel Type 2.

RESULTS:

Five cases were identified (4 men, 1 woman; mean age: 67.2 years). Four patients were referred for chronic or nonresolving CSC, and the diagnosis of MacTel Type 2 was made based on multimodal imaging findings. One patient had advanced MacTel Type 2, and developed acute CSC. Regarding the MacTel Type 2 findings, all subjects presented perifoveal telangiectasia on fluorescein angiography, and four subjects showed intraretinal cavitations typical of MacTel Type 2 on optical coherence tomography, in one or both eyes. Regarding the CSC findings, fluorescein angiography identified focal or extended retinal pigment epithelium alteration in all eyes, and an active leakage in two eyes. Indocyanine green angiography showed choroidal vascular hyperpermeability in four subjects. On optical coherence tomography, pigment epithelial detachments were detected in five eyes (four subjects), and foveal detachments were present in five eyes (three subjects), which spontaneously resolved (two eyes), responded to photodynamic therapy (two eyes), or persisted (one eye). Mean choroidal thickness was 402 ± 99 μm.

CONCLUSION:

The codiagnosis of CSC and MacTel Type 2 should be considered in atypical presentations associating features from both disorders.

PMID:
29016451
PMCID:
PMC5726910
[Available on 2019-01-01]
DOI:
10.1097/IAE.0000000000001836
[Indexed for MEDLINE]

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