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Pediatr Emerg Med Pract. 2016 Nov 22;13(11 Suppl Points & Pearls):S1-S2.

Managing acute complications of sickle cell disease in pediatric patients [digest].

Author information

1
Pediatric Emergency Medicine Fellow, Pediatric Emergency Medicine Department, SUNY Downstate Medical Center/Kings County Hospital Center, New York, NY.
2
Clinical Assistant Professor, Pediatric Emergency Medicine Department, SUNY Downstate Medical Center/Kings County Hospital Center, New York, NY.
3
Pediatric Emergency Medicine Fellow, Division of Emergency Medicine, Boston Children's Hospital, Boston, MA.

Abstract

Sickle cell disease is a chronic hematologic disease with a variety of acute, and often recurring, complications. Vaso-occlusive crisis, a unique but common presentation in sickle cell disease, can be challenging to manage. Acute chest syndrome is the leading cause of death in patients with sickle cell disease, occurring in more than half of patients who are hospitalized with a vaso-occlusive crisis. Uncommon diagnoses in children, such as stroke, priapism, and transient red cell aplasia, occur more frequently in patients with sickle cell disease and necessitate a degree of familiarity with the disease process and its management. Patients with sickle cell trait generally have a benign course, but are also subject to serious complications. This issue provides a current review of evidence-based management of the most common acute complications of sickle cell disease seen in pediatric patients in the emergency department. [Points & Pearls is a digest of Pediatric Emergency Medicine Practice].

PMID:
28745855
[Indexed for MEDLINE]

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