Format

Send to

Choose Destination
Ann Hepatol. 2017 May - Jun;16(3):460-464. doi: 10.5604/16652681.1235492.

Recurrent Hyperammonemia After Abernethy Malformation Type 2 Closure: a Case Report.

Author information

1
Department of gastroenterology, Shengjing Hospital Affiliated to China Medical University, Shenyang, Liaoning, China.

Abstract

The Abernethy malformation is a rare congenital malformation defined by the presence of an extrahepatic portosystemic shunt. Although most patients are asymptomatic, clinical encephalopathy is present in 15% of cases. We present a patient with type 2 Abernethy malformation, hyperammonemia, and encephalopathy. Shunt closure was performed successfully using interventional angiography; however, hyperammonemia recurred 3 months later. The diagnosis of Abernethy malformation can be made easily, but the ideal patient management strategy has not yet been established. This is the first reported patient with recurrence of hyperammonemia after interventional treatment; we discuss the therapeutic options for Abernethy malformation.

PMID:
28425418
DOI:
10.5604/16652681.1235492
[Indexed for MEDLINE]
Free full text

Supplemental Content

Full text links

Icon for IndexCopernicus
Loading ...
Support Center