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Acta Clin Belg. 2016 Aug 4:1-3. [Epub ahead of print]

Prosopagnosia as unusual presentation of semantic dementia: a case study.

Author information

1
a IRCCS Centro Neurolesi "Bonino Pulejo" , Messina , Italy.
2
b Department of Biomedical and Dental Sciences and Morphofunctional Imaging , University of Messina , Messina , Italy.

Abstract

OBJECT:

Semantic dementia is one of the main clinical variants of frontotemporal dementia and it is characterized by severe loss of conceptual knowledge with relative preservation of other cortical abilities.

METHODS:

We described a case of a patient affected by right temporal variant of frontotemporal lobar degeneration, characterized by prosopagnosia as an unusual disease onset.

RESULTS:

The neuropsychological evaluation showed a progressive deficit in face recognition and a slow decline in language in the absence of behavioral alterations. Magnetic resonance imaging showed diffuse vascular ischemic lesions, cortical atrophy in bilateral temporal lobes, and a marked bilateral decrease hippocampal volume, mainly involving the right side.

CONCLUSIONS:

Our findings suggest that prosopagnosia could be a predictive marker of atypical semantic dementia onset.

KEYWORDS:

Frontotemporal lobar degeneration; Hippocampus atrophy; Prosopagnosia; Semantic dementia

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