Pneumothorax in cystic fibrosis: beyond the guidelines

Robert W Lord; Andrew M Jones; A Kevin Webb; Peter J Barry

doi:10.1016/j.prrv.2016.06.012

Pneumothorax in cystic fibrosis: beyond the guidelines

Paediatr Respir Rev. 2016 Aug:20 Suppl:30-3. doi: 10.1016/j.prrv.2016.06.012. Epub 2016 Jun 15.

Authors

Robert W Lord¹, Andrew M Jones¹, A Kevin Webb¹, Peter J Barry²

Affiliations

¹ Manchester Adult Cystic Fibrosis Centre, University Hospital of South Manchester, Southmoor Road, Wythenshawe, M23 9LT, United Kingdom; Institute of Inflammation and Repair, University of Manchester, United Kingdom.
² Manchester Adult Cystic Fibrosis Centre, University Hospital of South Manchester, Southmoor Road, Wythenshawe, M23 9LT, United Kingdom; Institute of Inflammation and Repair, University of Manchester, United Kingdom. Electronic address: peter.barry@uhsm.nhs.uk.

PMID: 27374621
DOI: 10.1016/j.prrv.2016.06.012

Abstract

Pneumothorax is a serious but common complication in patients with cystic fibrosis (CF). It has adverse prognostic implications as well as associations with subsequent reduction in lung function and significant risk of recurrence. Management dilemmas frequently occur that are beyond current guidelines. We review the evidence and highlight management difficulties in pneumothoraces in CF.

Keywords: Cystic Fibrosis; Persistent air leak; Pleural intervention; Pleurodesis; Pneumothorax.

Publication types

Case Reports
Review

MeSH terms

Adolescent
Cystic Fibrosis / complications*
Cystic Fibrosis / microbiology
Cystic Fibrosis / physiopathology
Diagnostic Imaging
Disease Management
Humans
Male
Pneumothorax / diagnostic imaging
Pneumothorax / etiology*
Pneumothorax / physiopathology
Pneumothorax / therapy*
Prognosis
Respiratory Function Tests
Risk Factors