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Rev Chil Pediatr. 2016 Sep - Oct;87(5):366-372. doi: 10.1016/j.rchipe.2016.03.001. Epub 2016 Apr 15.

[Comparative results of Fontan surgery in patients with and without hypoplastic left heart syndrome].

[Article in Spanish]

Author information

1
División de Enfermedades Cardiovasculares, Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile. Electronic address: pbecker@med.puc.cl.
2
Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile.
3
División de Pediatría, Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile.
4
División de Enfermedades Cardiovasculares, Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile.

Abstract

INTRODUCTION:

During the last few years, numerous patients with univentricular heart disease have been treated surgically with total cavopulmonary anastomosis according to a staged surgery protocol in our institution.

OBJECTIVE:

To evaluate the perioperative outcomes and survival of patients with hypoplastic left heart syndrome (HLHS) after the Fontan procedure and compare them with other types of univentricular heart disease.

PATIENTS AND METHOD:

A total of 102 patients underwent a Fontan procedure between April 1996 and March 2014, 25 with HLHS (group I), and 77 patients with other types of univentricular heart disease (group II). Groups survival, demographics, hemodinamic studies, morbimortality, mechanical ventilation, surgical drains, post-operative stay, isotopes score, pacemaker use, and requiriment of Fontan takedown were analyzed.

RESULTS:

Intraoperative mortality was 4% (n=1) for group I, and 7.8% (n=6) for group II (P=.451). A difference was only found in hospital length of stay (LOS), being 17 days (6-47) for group I and 12 days (5-103) for group II (P=.017). Mean follow-up was 4.24±2.08 years for group I, and 8.7±4.67 for group II. Survival rate at 8 years for both groups was 88%, and 81% at 10 years for group II.

CONCLUSIONS:

The Fontan procedure had similar mortality, but longer LOS, in patients with HLHS compared to those with another types of single ventricle anatomy. Long term survival was comparable between both groups.

KEYWORDS:

Cardiopatías congénitas; Cirugía Fontan; Congenital heart defects; Fontan procedure; Hypoplastic left heart syndrome; Mortalidad; Mortality; Síndrome de corazón izquierdo hipoplásico

PMID:
27091396
DOI:
10.1016/j.rchipe.2016.03.001
[Indexed for MEDLINE]
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