Inhibition of oxygen-linked anion binding in Hb Camperdown [alpha 2 beta 2(104)(G6)Arg----Ser]

Hemoglobin. 1989;13(6):567-78. doi: 10.3109/03630268908993107.

Abstract

Oxygen equilibrium studies of purified Hb Camperdown [beta 104(G6) Arg----Ser] have revealed an increased oxygen affinity at acid pH, while it is decreased for pH values above 7.4. This accounts for an almost 40% reduction in the alkaline Bohr effect. The effects of chloride and organophosphate effectors on the oxygen affinity of Hb Camperdown are inhibited by 40-50%. In chloride-free Hepes buffer, Hb Camperdown exhibits a lower oxygen affinity than normal Hb A. The present results confirm the important role of the positively charged residues lining the beta 1 beta 2 interface in regulating the functional properties of hemoglobin.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • 2,3-Diphosphoglycerate
  • Anions / metabolism*
  • Chlorides / pharmacology
  • Diphosphoglyceric Acids / pharmacology
  • Hemoglobinopathies / blood
  • Hemoglobinopathies / genetics
  • Hemoglobins, Abnormal / genetics
  • Hemoglobins, Abnormal / metabolism*
  • Humans
  • Hydrogen-Ion Concentration
  • Male
  • Middle Aged
  • Oxidation-Reduction
  • Oxygen / metabolism*
  • Phytic Acid / pharmacology
  • Polycythemia / blood
  • Polycythemia / genetics

Substances

  • Anions
  • Chlorides
  • Diphosphoglyceric Acids
  • Hemoglobins, Abnormal
  • 2,3-Diphosphoglycerate
  • hemoglobin Camperdown
  • Phytic Acid
  • Oxygen