How strict is galactose restriction in adults with galactosaemia? International practice

Mol Genet Metab. 2015 May;115(1):23-6. doi: 10.1016/j.ymgme.2015.03.008. Epub 2015 Apr 7.

Abstract

Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides ± fruits and vegetables and 12 offal. 38% (n=15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n=13) or 2) giving fruits, vegetables and galactosides (n=2). Only 15% (n=6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation.

Keywords: Diet; Galactosaemia; Galactose; Galactose-1-phosphate; Lactose; Monitoring.

Publication types

  • Comparative Study
  • Multicenter Study

MeSH terms

  • Adult
  • Diet*
  • Food
  • Fruit
  • Galactose / administration & dosage*
  • Galactosemias / diet therapy*
  • Humans
  • Lactose / administration & dosage
  • Surveys and Questionnaires
  • Vegetables

Substances

  • Lactose
  • Galactose