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J Clin Neurosci. 2015 Jun;22(6):951-4. doi: 10.1016/j.jocn.2014.11.025. Epub 2015 Mar 9.

Hirayama disease.

Author information

1
Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia. Electronic address: dr.ecfoster@gmail.com.
2
Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia.
3
Department of Radiology, The Alfred Hospital, Melbourne, VIC, Australia.
4
Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia; Monash University, Melbourne, VIC, Australia.

Abstract

This article discusses three patients with likely Hirayama disease. They have no other significant past medical history and no personal or family history of other neurological disorders. Hirayama disease is a form of cervical myelopathy attributed to forward displacement of the posterior cervical dural sac on neck flexion with resultant cord compression and/or venous congestion. It is characterized by a pure motor focal amyotrophy in the distribution of C7, C8 and T1 spinal segmental-innervated muscles and differs from other motor neuron diseases by virtue of its ultimately non-progressive course.

KEYWORDS:

Cervical myelopathy; Hirayama disease; Motor focal amyotrophy; Motor neuron disease

PMID:
25766368
DOI:
10.1016/j.jocn.2014.11.025
[Indexed for MEDLINE]

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