Thrombasthenia is a congenital platelet disorder characterized by the normal platelet count, prolonged bleedingtime, absence of platelet aggregation and defective clot retraction. Clinically, purpura, epistaxis, gingival bleeding and excessive bleeding after minor injuries or operations are the main manifestations. We experienced a case of a 15-year-old boy suffering from thrombasthenia required extraction of 6/6. The problems of nature of the disease and its familial character are described and the problems of management are outlined.