Association of aortic and main left coronary aneurysms with severe aortic insufficiency in Takayasu's arteritis

Clin Pract. 2011 Apr 22;1(2):e26. doi: 10.4081/cp.2011.e26. eCollection 2011 May 16.

Abstract

Takayasu's arteritis is a granulomatous vasculitis of unknown etiology that affects mainly the aorta and its branches. As a result of intimal fibroproliferation, segmental stenosis, occlusion, dilatation, and aneurysmal formation of the involved vessels may develop. It is an uncommon disease and usually affects young Asian female patients during the second and third decades of life. Coronary arteries are exceptionally affected and coronary aneurysm formation is a very rare finding. We describe a case of a previously healthy 26-year-old Caucasian female whose Takayasu's arteritis presented as a previously undescribed association of aortic and main left coronary aneurysms with severe aortic insufficiency.

Keywords: Takayasu’s arteritis; aneurysm; aortitis.; coronary artery; vasculitis.

Publication types

  • Case Reports