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J Korean Med Sci. 2014 Apr;29(4):609-13. doi: 10.3346/jkms.2014.29.4.609. Epub 2014 Apr 1.

Pneumonectomy case in a newborn with congenital pulmonary lymphangiectasia.

Author information

1
Department of Pediatrics, Eulji University College of Medicine, Daejeon, Korea.
2
Department of Thorasic and Cardiovascular Surgery, Eulji University College of Medicine, Daejeon, Korea.
3
Department of Pathology, Eulji University College of Medicine, Daejeon, Korea.
4
Department of Radiology, Eulji University College of Medicine, Daejeon, Korea.

Abstract

Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ventilator care. Right pneumonectomy was performed after her symptoms worsened. Histologic examination indicated CPL. She is currently 12 months old and developing normally. Pneumonectomy can be considered for treating respiratory symptoms for improving chances of survival in cases with unilateral CPL.

KEYWORDS:

Infant, Newborn; Lymphangiectasia, Pulmonary, Congenital; Pneumonectomy

PMID:
24753713
PMCID:
PMC3991809
DOI:
10.3346/jkms.2014.29.4.609
[Indexed for MEDLINE]
Free PMC Article

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