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Ann Pathol. 2014 Feb;34(1):14-25. doi: 10.1016/j.annpat.2014.01.012. Epub 2014 Feb 25.

[Peritoneal pseudomyxoma: an overview emphasizing pathological assessment and therapeutic strategies].

[Article in French]

Author information

1
Département d'anatomie pathologique, institut Gustave-Roussy, 94805 Villejuif, France.
2
Service d'anatomie pathologique, centre hospitalier Lyon-Sud, hospices civils de Lyon, 69495 Pierre-Bénite, France.
3
Pôle information médicale, unité de recherche clinique, hospices civils de Lyon, 69495 Lyon, France.
4
Service de chirurgie générale et digestive, centre hospitalier Lyon-Sud, hospices civils de Lyon, 69495 Pierre-Bénite, France.
5
Département d'anatomie pathologique, centre François-Baclesse, 14076 Caen, France.
6
Service d'anatomie pathologique, CHU l'Archet II, 06200 Nice, France.
7
Département d'anatomie pathologique, institut Bergonié, 33076 Bordeaux, France.
8
Service d'anatomie pathologique, CHU Lariboisière, 75010 Paris, France.
9
Service d'anatomie pathologique, CHRU de Hautepierre, 67091 Strasbourg, France.
10
Service d'anatomie pathologique, CHU Albert-Michallon, 38043 Grenoble, France.
11
Département d'anatomie pathologique, institut de cancérologie de Lorraine, 54519 Vandœuvre-lès-Nancy, France.
12
Département d'anatomie pathologique, institut Claudius-Regaud, 31052 Toulouse, France.
13
Département d'anatomie pathologique, institut Paoli-Calmettes, 13273 Marseille, France.
14
Service d'anatomie pathologique, CHU Jean-Minjoz, 25030 Besançon, France.
15
Service d'anatomie pathologique, centre Paul-Papin, 49933 Angers, France.
16
Service d'anatomie pathologique, Institut Régional du Cancer de Montpellier-Val d'Aurelle, 34298 Montpellier, France. Electronic address: frederic.bibeau@icm.unicancer.fr.

Abstract

Pseudomyxoma peritonei is a clinical entity characterized by a gelatinous ascite associated with mucinous tumor deposits spreading on peritoneal surface and potentially invading abdominal organs. It is considered as a tumor process linked, in most of cases, to a mucinous appendiceal neoplasm. Pseudomyxoma peritonei may benefit from a therapeutic strategy combining cytoreductive surgery and intra-peritoneal chemotherapy, which has led to a major prognosis improvement. Different classifications are available and the last one corresponds to the WHO 2010 version, which individualizes pseudomyxoma peritonei in two classes: low grade and high grade mucinous carcinoma. The very low frequency of this entity and its specific therapeutic strategy need specific health care centres, as well as physicians and pathologists collaborating through dedicated networks. The aim of this article is to summarize the pathology, causes, mechanisms and therapeutic approaches of pseudomyxoma peritonei, as well as their interfaces with dedicated networks.

KEYWORDS:

Appendice; Networks; Pseudomyxoma peritonei; Pseudomyxomes péritonéaux; Rares tumors; Réseaux; Tumeurs rares

PMID:
24630633
DOI:
10.1016/j.annpat.2014.01.012
[Indexed for MEDLINE]

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