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J Pediatr Adolesc Gynecol. 2014 Aug;27(4):e79-81. doi: 10.1016/j.jpag.2013.07.009. Epub 2013 Nov 20.

Delayed diagnosis of Herlyn-Werner-Wunderlich syndrome due to microperforation and pyocolpos in obstructed vaginal canal.

Author information

1
Department of Gynecology, Medical University of Lublin, Lublin, Poland. Electronic address: ewa.wozniakowska@gmail.com.
2
Department of Human Anatomy, Medical University of Lublin, Lublin, Poland.
3
Department of Gynecology, Medical University of Lublin, Lublin, Poland.

Abstract

BACKGROUND:

To present a rare anomaly consisting of uterus didelphys, longitudinal vaginal septum, obstructed hemivagina with pyocolpos, fistula to the open vaginal canal, and ipsilateral renal agenesis, referred as Herlyn-Werner-Wunderlich syndrome (HWWS).

CASE:

A 14-year-old girl with recurring purulent vaginal discharge lasting for a few months. Preoperative examination revealed one vaginal canal with one cervical opening on the right side. There was a fistula leading from the obstructed vaginal canal to the left vagina. Intravaginal ultrasound examination demonstrated a longitudinal vaginal septum and a closed pyocolpos on the right side. The longitudinal vaginal septum was excised by way of electrocauterization under direct vision.

CONCLUSION:

HWWS should be considered in the differential diagnosis in patients with uterus didelphys and unusual symptoms such as pyocolpos and vaginal discharge.

KEYWORDS:

Fistula; Herlyn-Werner-Wunderlich syndrome; Longitudinal vaginal septum; Purulent vaginal discharge; Pyocolpos

PMID:
24268556
DOI:
10.1016/j.jpag.2013.07.009
[Indexed for MEDLINE]

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