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J Mal Vasc. 2014 Feb;39(1):67-72. doi: 10.1016/j.jmv.2013.10.002. Epub 2013 Nov 6.

[Secretan's syndrome: myth or pathomimia?].

[Article in French]

Author information

1
Clinique de médecine vasculaire, clinique universitaire de médecine vasculaire, CHU de Grenoble, BP 217, 38043 Grenoble cedex 09, France.
2
Clinique de chirurgie de la main, CHU de Grenoble, 38043 Grenoble cedex 09, France.
3
Clinique de médecine vasculaire, clinique universitaire de médecine vasculaire, CHU de Grenoble, BP 217, 38043 Grenoble cedex 09, France. Electronic address: SBlaise@chu-grenoble.fr.

Abstract

Secretan's syndrome is a rare condition involving generally trauma-induced hard edema of the dorsal aspect of the hand. The cause is poorly understood but factitious trauma is often suspected.

CASE REPORT:

A 42-year-old woman presented with a fortuitous edema on the back of the right hand. The minimally depressible edema was associated with moderately intense mechanical pain. Routine laboratory tests were normal. An extensive imaging work-up (bone x-ray of the hand and wrist, bone scintigraphy, computed tomography phlebography, lymphoscintigraphy, magnetic resonance imaging) was equally non-contributive. The diagnosis of self-inflected trauma was suggested by the atypical nature of the edema, the absence of any organic disorder on the tests performed, and the patient's attitude concerning her disease. In this clinical context, the diagnosis of Secretan's syndrome was retained. Outcome was compatible, with secondary development of complex regional pain syndrome.

DISCUSSION:

Three forms of Secretan's syndrome have been recently described: benign; hyperplastic; and mixed. The cause remains poorly defined. Certain authors report that it is most likely related to pathomimia. Treatment can combine physiotherapy and psychological counseling.

CONCLUSION:

Secretan's syndrome is a poorly-understood and rarely-described condition that may be underdiagnosed. Physicians specialized in vascular medicine should be aware of this syndrome and its difficult diagnosis by elimination.

KEYWORDS:

Factitious lymphedema; Lymphœdème; Pathomimia; Pathomimie; Secretan's syndrome; Syndrome de Secrétan

PMID:
24210749
DOI:
10.1016/j.jmv.2013.10.002
[Indexed for MEDLINE]
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