Reversal of Young's procedure in hereditary haemorrhagic telangiectasia

J Laryngol Otol. 2012 Nov;126(11):1169-71. doi: 10.1017/S0022215112001806. Epub 2012 Aug 29.

Abstract

Background: Hereditary haemorrhagic telangiectasia is an autosomal dominant condition characterised by multiple venous malformations of the skin and mucous membranes which can bleed on contact. A Young's procedure is used to control severe epistaxis in patients with this condition. However, there has been no previous report of a reversal of Young's procedure in such a patient.

Objective: A patient with hereditary haemorrhagic telangiectasia had his Young's procedure reversed under general anaesthetic by dividing the mucocutaneous flaps. Nasal vestibule patency was maintained using a custom-made silicone nasal mould. Intra-operative photographs show the patient's nasal mucosa shortly following reversal of his Young's procedure, and also illustrate the creation of the custom-made nasal mould.

Conclusion: Stopping airflow through the nasal cavity via a Young's procedure prevents the telangiectasia from bleeding but does not make them disappear completely. Young's procedure does not seem to have any long-lasting effect on the nasal mucosa of patients with hereditary haemorrhagic telangiectasia.

Publication types

  • Case Reports

MeSH terms

  • Epistaxis / surgery*
  • Humans
  • Male
  • Middle Aged
  • Nasal Cavity / surgery*
  • Telangiectasia, Hereditary Hemorrhagic / surgery*
  • Treatment Outcome