Format

Send to

Choose Destination
BMC Med. 2012 Aug 10;10:88. doi: 10.1186/1741-7015-10-88.

State of progress in treating cystic fibrosis respiratory disease.

Author information

1
Medical University of South Carolina, Charleston, SC, USA. flumepa@musc.edu

Abstract

Since the discovery of the gene associated with cystic fibrosis (CF), there has been tremendous progress in the care of patients with this disease. New therapies have entered the market and are part of the standard treatment of patients with CF, and have been associated with marked improvement in survival. Now there are even more promising therapies directed at different components of the pathophysiology of this disease. In this review, our current knowledge of the pathophysiology of lung disease in patients with CF is described, along with the current treatment of CF lung disease, and the therapies in development that offer great promise to our patients.

PMID:
22883684
PMCID:
PMC3425089
DOI:
10.1186/1741-7015-10-88
[Indexed for MEDLINE]
Free PMC Article

Supplemental Content

Full text links

Icon for BioMed Central Icon for PubMed Central
Loading ...
Support Center