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An Bras Dermatol. 2011 Nov-Dec;86(6):1222-3.

Case for diagnosis. Acrokeratoelastoidosis.

[Article in English, Portuguese]

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Prof. Rubem David Azulay Institute of Dermatology, Santa Casa de Miseric├│rdia do Rio de Janeiro, Brazil.


Acrokeratoelastoidosis is a type of palmoplantar keratoderma first described by Oswaldo Gon├žalves Costa, a Brazilian Dermatologist from the state of Minas Gerais. It is a rare autosomal-dominant genodermatosis; however it may occur sporadically. The disease is not congenital; rather, its onset occurs in childhood or adolescence. Clinically, the condition is characterized by multiple yellowish papules, sometimes glossy and keratotic, measuring approximately 2-4 mm in diameter, sometimes umbilicated, and located symmetrically on the sides of the hands and feet, symmetry being the most typical sign. The most common histopathological findings are hyperkeratosis, mild acanthosis and elastorrhexis, as revealed by orcein staining.

[Indexed for MEDLINE]

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