Partial nephrectomy for a large renal lymphatic malformation in a child presenting with hypertension

Wai Lee; Praneeth Vemulapalli; Frederick Miller; Jonathan Melquist; Thomas K Lee; Frank S Darras

doi:10.1016/j.jpedsurg.2011.10.003

Partial nephrectomy for a large renal lymphatic malformation in a child presenting with hypertension

J Pediatr Surg. 2012 Jan;47(1):e23-6. doi: 10.1016/j.jpedsurg.2011.10.003.

Authors

Wai Lee¹, Praneeth Vemulapalli, Frederick Miller, Jonathan Melquist, Thomas K Lee, Frank S Darras

Affiliation

¹ Department of Urology, Stony Brook University Medical Center, Stony Brook, NY 11794, USA. wai.lee.8@hsc.stonybrook.edu

PMID: 22244432
DOI: 10.1016/j.jpedsurg.2011.10.003

Abstract

A 9-year-old girl had hypertension (systolic blood pressure of 125 mm Hg) noted at an annual well child visit. An ultrasound study demonstrated a large right renal cystic mass. A partial nephrectomy was performed. The surgical specimen was 9.7 × 9.4 × 6.4 cm and weighed 413.2 g. The tumor stained diffusely positive for smooth muscle actin and focally positive for factor VIII. Final histologic diagnosis was primary intrarenal lymphatic malformation. The case is unusual because of the presentation, size of the mass, as well as the therapeutic approach of partial nephrectomy.

Publication types

Case Reports

MeSH terms

Child
Female
Humans
Hypertension / etiology
Kidney*
Lymphatic Abnormalities / complications
Lymphatic Abnormalities / diagnosis
Lymphatic Abnormalities / surgery*
Nephrectomy / methods*