Format

Send to

Choose Destination
See comment in PubMed Commons below
Turk Neurosurg. 2011;21(4):651-4. doi: 10.5137/1019-5149.JTN .2989-10.1.

Lhermitte - Duclos disease with syrinx: case report and literature review.

Author information

1
SKIMS, Department of Neurosurgery, Kashmir, India.

Abstract

BACKGROUND:

Lhermitte-Duclos disease is typified by a hamartomatous lesion of the cerebellum. It is usually seen in females. The usual presentation is of raised intracranial pressure along with cerebellar signs.

CASE REPORT:

We report an 18-year-old female patient who presented to us with history of headache and gait ataxia and was observed to have Lhermitte-Duclos disease with cervical cord syrinx on imaging.

DISCUSSION:

To our knowledge this is the fifth case of Lhermitte-Duclos disease with syringomyelia in the pediatric age group. The treatment of this condition is decompression of the lesion. Malignant transformation never occurs and the prognosis is excellent.

[Indexed for MEDLINE]
Free full text
PubMed Commons home

PubMed Commons

0 comments
How to join PubMed Commons

    Supplemental Content

    Full text links

    Icon for Turkish Neurosurgical Society
    Loading ...
    Support Center