Format

Send to

Choose Destination
Pediatr Radiol. 2011 Aug;41(8):985-92. doi: 10.1007/s00247-011-2124-1. Epub 2011 Jun 10.

Mediastinal involvement in lymphangiomatosis: a previously unreported MRI sign.

Author information

1
Department of Radiology, Great Ormond Street Hospital for Children, London, WC1N 3JH, UK. vikasshah@yahoo.com

Abstract

BACKGROUND:

Multifocal lymphangiomatosis is a rare systemic disorder affecting children. Due to its rarity and wide spectrum of clinical, histological and imaging features, establishing the diagnosis of multifocal lymphangiomatosis can be challenging.

OBJECTIVES:

The purpose of this study was to describe a new imaging sign in this disorder: paraspinal soft tissue and signal abnormality at MRI.

MATERIALS AND METHODS:

We retrospectively reviewed the imaging, clinical and histopathological findings in a cohort of eight children with thoracic involvement from this condition.

RESULTS:

Evidence of paraspinal chest disease was identified at MRI and CT in all eight of these children. The changes comprise heterogeneous intermediate-to-high signal parallel to the thoracic vertebrae on T2-weighted sequences at MRI, with abnormal paraspinal soft tissue at CT and plain radiography.

CONCLUSION:

Multifocal lymphangiomatosis is a rare disorder with a broad range of clinicopathological and imaging features. MRI allows complete evaluation of disease extent without the use of ionising radiation and has allowed us to describe a previously unreported imaging sign in this disorder, namely, heterogeneous hyperintense signal in abnormal paraspinal tissue on T2-weighted images.

PMID:
21660638
DOI:
10.1007/s00247-011-2124-1
[Indexed for MEDLINE]

Supplemental Content

Full text links

Icon for Springer
Loading ...
Support Center