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Neuroradiology. 1990;32(4):328-30.

MRI findings in the mild type of mucopolysaccharidosis II (Hunter's syndrome).

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Department of Neurology, Juntendo University School of Medicine, Tokyo, Japan.


Neuroradiological findings in a 44-year-old male with the typical mild type of Hunter's disease are reported. Cranial MRI revealed patchy areas of increased and decreased signals in T1- and T2-weighted images in the thalamus and the basal ganglia giving rise to a honey comb-like appearance as a whole. The deep white matter showed high signals in the T2-weighted image. To our knowledge, the honey comb-like appearance has never been reported in this disorder. Deposition of mucopolysaccharides and/or glycolipids and increase in fluid content seem to be responsible for these changes.

[Indexed for MEDLINE]

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