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Arch Neurol. 2010 Aug;67(8):1012-5. doi: 10.1001/archneurol.2010.187.

Bilateral pallidal stimulation for x-linked dystonia parkinsonism.

Author information

1
Movement Disorders Centre, Toronto Western Hospital, 399 Bathurst St, McL7-402, Toronto, Ontario, Canada, M5T 2S8. elena.moro@uhn.on.ca.

Erratum in

  • Arch Neurol. 2011 Jun;68(6):724. Diaz, Cristina Torres [corrected to Torres Diaz, Cristina V].

Abstract

OBJECTIVE:

To report the clinical benefits of bilateral deep brain stimulation (DBS) of the globus pallidus internus (GPi) in a patient with X-linked dystonia parkinsonism (XDP).

DESIGN:

Case report.

SETTING:

Tertiary referral center. Patient A 40-year-old Filipino man with genetically confirmed XDP and severely disabling generalized dystonia. Intervention Bilateral GPi DBS.

MAIN OUTCOME MEASURES:

The primary outcome measures were the Burke-Fahn-Marsden Dystonia Scale (BFMDS) severity and disability scores, and the secondary outcome measure was the Unified Parkinson Disease Rating Scores.

RESULTS:

At the 1-year postoperative follow-up, there was 80.4% improvement in the BFMDS severity score and 66.7% improvement in the BFMDS disability score.

CONCLUSION:

Bilateral GPi DBS seems to be very effective in improving dystonia in XDP.

PMID:
20697054
DOI:
10.1001/archneurol.2010.187
[Indexed for MEDLINE]

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