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Kardiol Pol. 2010 Mar;68(3):304-9.

The diagnosis, clinical course and follow-up of children with cardiac tumours - a single-centre experience.

Author information

1
Department of Paediatric cardiology, Silesian Paediatric Medical Center, Katowice, Poland. jkohut6@wp.pl

Abstract

BACKGROUND:

Rhabdomyoma is the most frequent primary cardiac tumour in children (about 50% of all cardiac neoplasms in this population). Fibroma, myxoma, teratoma and haemangioma are less frequent.

AIM:

To investigate the clinical presentation, diagnosis and follow-up of children diagnosed with cardiac tumours in our department between 1993 and 2008.

METHODS:

In the 15-year review we found 9 cases of cardiac tumours, confirmed in echo scan in every case and pathomorphologically in 5 out of 9 cases.

RESULTS:

Cardiac tumours were found in six boys and three girls, usually in the neonatal period. Cardiac murmur was the most common clinical symptom (4 cases). Two children were symptom-free. Out of the remaining children, two had circulatory failure and one had arrhythmia. Five children were operated on: three cases of rhabdomyoma, one fibroma and one teratoma. In 3 children who did not undergo surgery, the most probable diagnosis was rhabdomyoma. The follow-up (possible in 8 out of 9 cases, mean 7 years) showed that six children developed regularly and in two cases neurological abnormalities appeared.

CONCLUSIONS:

In this series, primary cardiac tumours presented as murmurs or circulatory failure. Most children needed surgery. In most cases, pathomorphology revealed rhabdomyoma. Follow-up showed regular development in six out of nine cases.

PMID:
20411454
[Indexed for MEDLINE]

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