Send to

Choose Destination
Indian J Dermatol. 2009;54(4):378-9. doi: 10.4103/0019-5154.57619.

Hyper IgE syndrome with umbilical hernia.

Author information

Department of Dermatology, Dr. B.R. Ambedkar Medical College and Hospital, K.G. Halli, Bangalore - 560 045, Karnataka, India.


Hyper IgE Syndrome (HIES) is a rare multi system genetic immunodeficiency disorder, with immunological and non-immunological features. Immunolgical features are 1) Recurrent cutaneous abscesses, 2) Atopic dermatitis like lesions, 3) Sino pulmonary infections, 4) Elevated serum IgE levels and 5) Abnormal neutrophil chemotaxis. Non immunological features include cranio facial and skeletal abnormalities. We are reporting a girl with classical features of HIES with umbilical hernia with her younger brother suffering from right sided inguinal hernia, as both herniae are hitherto unreported in patients with HIES.


Hyper IgE syndrome; inguinal hernia; umbilical hernia

Supplemental Content

Full text links

Icon for Medknow Publications and Media Pvt Ltd Icon for PubMed Central
Loading ...
Support Center