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Pediatr Blood Cancer. 2010 Jan;54(1):170-2. doi: 10.1002/pbc.22281.

Successful radiation therapy for supratentorial primitive neuroectodermal tumor and epidermolysis bullosa simplex.

Author information

1
Department of Radiation Oncology, Childrens Hospital Los Angeles, Los Angeles, California, USA.

Abstract

Epidermolysis bullosa simplex (EBS) is a heritable skin disorder characterized by skin fragility and blistering. While its most severe variant, dystrophic epidermolysis bullosa (DEB) is associated with squamous cell carcinoma (SCC), the development of extracutaneous neoplasms in EBS is extremely rare. We report a novel case of supratentorial primitive neuroectodermal tumor (sPNET) in a 7-year male with EBS. Experience of radiation therapy and its challenges in children with EBS has rarely been reported.

PMID:
19760773
DOI:
10.1002/pbc.22281
[Indexed for MEDLINE]

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