Format

Send to

Choose Destination
See comment in PubMed Commons below
Urology. 2010 Jan;75(1):176-8. doi: 10.1016/j.urology.2009.04.073. Epub 2009 Jul 17.

Lipoid congenital adrenal hyperplasia: pathologic features of the testis.

Author information

1
Department of Urology, Chonnam National University Medical School, Gwangju, Korea.

Abstract

Lipoid congenital adrenal hyperplasia (lipoid CAH) is a rare disorder of steroid biosynthesis that is caused by a molecular defect in the steroidogenic acute regulatory protein. Patients with lipoid CAH usually experience life-threatening adrenal insufficiency and develop female external genitalia in both genetic sexes because of deficient gonadal steroid synthesis. Little is known regarding testicular histology in patients with lipoid CAH, and less is known about the changes in testicular histology with growth. This article describes testicular histopathology in a patient with 46, XY lipoid CAH who underwent orchiectomy at the age of 8 years.

PMID:
19616293
DOI:
10.1016/j.urology.2009.04.073
[Indexed for MEDLINE]
PubMed Commons home

PubMed Commons

0 comments
How to join PubMed Commons

    Supplemental Content

    Full text links

    Icon for Elsevier Science
    Loading ...
    Support Center