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J Korean Med Sci. 2009 Apr;24(2):346-9. doi: 10.3346/jkms.2009.24.2.346. Epub 2009 Apr 20.

Perivascular epithelioid cell tumor (PEComa) of abdominal cavity from falciform ligament: a case report.

Author information

1
Department of Internal Medicine, Pusan National University College of Medicine, Busan, Korea.

Abstract

We present a case of perivascular epithelioid cell tumors (PEComas) in the abdominal cavity at the falciform ligament. A 30-yr-old Korean man visited to hospital for the evaluation of a growing, palpable abdominal mass. He had felt the mass growing over 6 months. There was no family or personal history of tuberous sclerosis. The resected specimen showed a mass of 8.0x7.0x5.5 cm in size. Histological examination showed sheets of spindle-to-epithelioid cells with clear-to-eosinophilic cytoplasm. Immunohistochemically, tumor cells were positive for HMB-4 (gp100) and smooth muscle actin. They were also positive for the S-100, which is a marker of neurogenic and melanocytic tumors. Patient was treated with radical resection of tumor without any adjuvant therapy. He is well and on follow-up visits without tumor recurrence.

KEYWORDS:

Angiomyolipoma; Lymphangiomyomatosis; Perivascular Epithelioid Cell Neoplasms

PMID:
19399284
PMCID:
PMC2672142
DOI:
10.3346/jkms.2009.24.2.346
[Indexed for MEDLINE]
Free PMC Article

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