We present the case of 22-month-old boy with Urticaria pigmentosa. Clinical feature was presented as disseminated yellow-brownish patches, on the skin of entire body, including skin of the scalp, 1x2 cm in diameter. No subjective symptoms were present. First skin lesion occurred in the second month of life. Darier's sign was positive. Serum triptase levels were elevated. Diagnosis of mastocytosis was confirmed by pathohistology.