Format

Send to

Choose Destination
Acta Ortop Mex. 2007 Nov-Dec;21(6):338-43.

[Freeman-Sheldon's syndrome. Report of five cases].

[Article in Spanish]

Author information

1
Hospital Shriners para Niños, México, D.F. Clínica de Cirugía de Mano. vergarahenry@hotmail.com

Abstract

INTRODUCTION:

Freeman-Sheldon syndrome, described in 1938, is an infrequent form of arthrogryposis.

MATERIAL AND METHODS:

We reviewed the files of the patients with the diagnosis of Freeman-Sheldon syndrome from 1990 to 2003, and carried out an evaluation of the clinical data, family history and malformations of extremities.

RESULTS:

5 patients were included, 4 male and 1 female. Upper extremities: All patients presented adducted thumbs, 3 patients were treated with a first web release and dorsal graft with improvement of grip on larger objects. Feet: Four patients had severe bilateral rigid clubfeet, they were operated on with a posteromedial release and bilateral talectomy, satisfactory results were obtained in 4 of 6 feet according to Niki criteria. Other non orthopedic anomalies: In three patients unilateral right undescended testis; 1 right inguinal hernia.

CONCLUSIONS:

The patients have as common factor the whistler appearance, accompanied with mill crosses hand deformity, adducted thumbs, accompanied or not with inferior extremities deformities, intellectual capacity was normal.

PMID:
18386533
[Indexed for MEDLINE]
Free full text

Supplemental Content

Full text links

Icon for Graphimedic, S.A. de C.V.
Loading ...
Support Center