Format

Send to

Choose Destination
See comment in PubMed Commons below
Dev Neurosci. 1991;13(4-5):262-6.

Peroxisomal fatty acid beta-oxidation in relation to adrenoleukodystrophy.

Author information

1
Department of Pediatrics, University Hospital Amsterdam, The Netherlands.

Abstract

X-linked adrenoleukodystrophy is a neurological disease characterized by progressive demyelination with destruction of the white matter, and adrenal insufficiency. Biochemically there is accumulation of very-long-chain fatty acids resulting from an impairment in the peroxisomal oxidation of these fatty acids. In this paper we describe the present state of our knowledge with regard to the organization of the peroxisomal fatty acid oxidation system, with particular emphasis on X-linked adrenoleukodystrophy.

PMID:
1817031
[Indexed for MEDLINE]
PubMed Commons home

PubMed Commons

0 comments
How to join PubMed Commons

    Supplemental Content

    Loading ...
    Support Center