Format

Send to

Choose Destination
See comment in PubMed Commons below
J Neurol Sci. 2008 Apr 15;267(1-2):162-5. Epub 2007 Oct 26.

Dropped-head syndrome due to steroid responsive focal myositis: a case report and review of the literature.

Author information

1
Department of Neurology, University of Göttingen, Robert-Koch-Str. 40, 37075, Göttingen, Germany. andreas.kastrup@medizin.uni-goettingen.de

Abstract

Isolated severe weakness of the paraspinal musculature, either at the cervical level leading to a "dropped head syndrome" or at the thoracic level leading to a "bent-spine syndrome", is a rare disorder. Etiologically it may be present in a variety of neurological diseases including Parkinson's disease, multiple system atrophy, neuromuscular or motor neuron diseases, as well as non-inflammatory, inflammatory, dystrophic or metabolic myopathies. We present a previously healthy 74-year-old man with a 2-month history of progressive difficulty in lifting his chin off his chest. Magnetic resonance imaging and skeletal muscle biopsy revealed an isolated myositis of the neck extensor and trapezius muscles, which responded well to steroid therapy. This case and other rare reports obtained from a systematic review of the literature indicate that in a subgroup of patients "dropped head syndrome" or "bent spine syndrome" is caused by a myositis, which emphasizes the necessity to obtain a MRI examination, as well as a muscle biopsy to diagnose this potentially treatable disease.

PMID:
17964603
DOI:
10.1016/j.jns.2007.09.042
[Indexed for MEDLINE]
PubMed Commons home

PubMed Commons

0 comments
How to join PubMed Commons

    Supplemental Content

    Full text links

    Icon for Elsevier Science
    Loading ...
    Support Center