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Europace. 2007 Mar;9(3):162-6. Epub 2007 Feb 1.

Sudden cardiac death in Andersen-Tawil syndrome.

Author information

1
Klinikum Dorothea Christiane Erxleben Quedlinburg, Academic Teaching Hospital of the University Hospital Magdeburg, Innere Medizin II-Kardiologie, Ditfurter Weg 24, 06484 Quedlinburg, Germany. s.peters@klinikum-quedlinburg.de

Abstract

Andersen-Tawil syndrome (ATS) is an autosomal dominant or sporadic disorder characterized by periodic paralysis, dysmorphic features, and ventricular arrhythmias. Although ventricular tachycardia burden is quite high sudden cardiac death in ATS is rare. We describe a case with sudden cardiac death due to electrical storm a few days after ICD implantation in KCNJ2 mutation-negative ATS.

PMID:
17272325
DOI:
10.1093/europace/eul188
[Indexed for MEDLINE]

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