Format

Send to

Choose Destination
Klin Padiatr. 2006 Jul-Aug;218(4):224-5. Epub 2006 Mar 1.

[Congenital intestinal lymphangiectasia: a rare differential diagnosis in hypoproteinemia in infants].

[Article in German]

Author information

1
Westfälisches Kinderzentrum Dortmund, Klinikum Dortmund gGmbH, Beurhausstrasse 40, 44137 Dortmund. ansgar.moeller@klinikumdo.de

Abstract

BACKGROUND:

Congenital intestinal lymphangiectasia is a rare disease in childhood, which may already cause protein-losing enteropathy in newborns.

PATIENT, METHODS AND RESULTS:

This is a case report of an infant with generalized edema and protein-losing enteropathy, in whom intestinal lymphangiectasia was diagnosed at the age of two months. Following repetitive intravenous albumin und gamma globulin infusions, the elimination of long-chain fats from the diet and the substitution with medium-chain triglycerides (MCT) led to an improvement of the protein-losing enteropathy.

CONCLUSION:

In newborns with low level of serum protein and edema protein-losing enteropathy caused by congenital lymphangiectasia might be considered as a differential diagnosis.

PMID:
16586269
DOI:
10.1055/s-2006-921454
[Indexed for MEDLINE]

Supplemental Content

Full text links

Icon for Georg Thieme Verlag Stuttgart, New York
Loading ...
Support Center