Format

Send to

Choose Destination
See comment in PubMed Commons below
Dev Med Child Neurol. 2006 Mar;48(3):231-5.

Cardiac monitoring and treatment for children and adolescents with neuromuscular disorders.

Author information

1
Department of Congenital Cardiology, Yorkshire Heart Centre, Leeds General Infirmary, Leeds LS1 3EX, UK. kate.english@leedsth.nhs.uk

Abstract

Dilated cardiomyopathy, hypertrophic cardiomyopathy, and cardiac rhythm disturbances are important features of certain neuromuscular disorders in children, adolescents, and young adults. This article summarizes the cardiac features seen in patients with Duchenne muscular dystrophy, Becker muscular dystrophy, myotonic dystrophy, Friedreich's ataxia, and Emery-Dreifuss muscular dystrophy. The optimal management of these cardiac features remains contentious, but increasingly these patients are referred for routine cardiological assessment in the absence of symptoms. This article examines the value of routine screening and drug interventions for cardiac complications in asymptomatic and symptomatic individuals with neuromuscular disorders. We recommend a pragmatic approach, actively looking for cardiac conditions which will benefit from early intervention, but avoiding routine screening for asymptomatic conditions in which there is no evidence of benefit from early intervention.

PMID:
16483403
DOI:
10.1017/S0012162206000491
[Indexed for MEDLINE]
Free full text
PubMed Commons home

PubMed Commons

0 comments
How to join PubMed Commons

    Supplemental Content

    Full text links

    Icon for Wiley
    Loading ...
    Support Center