Benign ileocecal valve hypertrophy is a rare cause for intestinal obstruction. We describe a 51-year-old female with clinical and imaging presentation of chronic small-bowel obstruction. The patient was operated on, and a limited thickening of the ileocecal bowel wall causing intestinal obstruction was found. A right hemicolectomy was performed. On microscopic examination, severe fibrosis with hypertrophied nerves was found without any additional findings of malignancy or inflammation. Review of the relevant literature is presented.