Chronic granulomatous disease presenting with eosinophilic inflammation

Pediatr Infect Dis J. 2005 Nov;24(11):1020-1. doi: 10.1097/01.inf.0000183775.69035.33.

Abstract

Chronic granulomatous disease (CGD), a rare immunodeficiency, typically presents with recurrent infections caused by catalase-positive organisms. We report 2 patients with CGD who presented with eosinophilic inflammatory conditions recognized before the diagnosis of CGD. Both patients had significant urologic disease. Physicians should be aware of the association of CGD with eosinophilic inflammatory conditions.

Publication types

  • Case Reports

MeSH terms

  • Achromobacter denitrificans / enzymology
  • Achromobacter denitrificans / isolation & purification*
  • Aspergillosis / complications
  • Aspergillosis / diagnosis
  • Aspergillus / enzymology
  • Aspergillus / isolation & purification
  • Catalase / metabolism*
  • Child, Preschool
  • Eosinophils / immunology
  • Gram-Negative Bacterial Infections / complications
  • Gram-Negative Bacterial Infections / diagnosis
  • Granulomatous Disease, Chronic / immunology*
  • Granulomatous Disease, Chronic / microbiology*
  • Humans
  • Infant
  • Inflammation / immunology
  • Inflammation / microbiology*
  • Male

Substances

  • Catalase