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Jpn J Thorac Cardiovasc Surg. 2005 Aug;53(8):458-62.

Primary cardiac rhabdomyosarcoma following a uterine leiomyosarcoma: double primary sarcomas.

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Division of Cardiovascular Surgery, Cardiovascular Center, Sagamihara Kyodo Hospital, Sagamihara, Kanagawa, Japan.


Primary cardiac rhabdomyosarcoma is rare. A dismal prognosis is usually given due to its high propensity for distant metastases, with survival rarely exceeding 2 years. We report a case that was initially considered to be a cardiac metastatic tumor from a primary uterine leiomyosarcoma, but after morphological and immunohistochemical examinations was shown to be a primary cardiac rhabdomyosarcoma. The right atrium was filled with a mass that oscillated between the right atrium and ventricle through the tricuspid valve. To reduce the risk of sudden death from tumor embolism into the pulmonary arteries, the tumor was resected. Even though the surgery was not curative, it eliminated the risk of sudden death due to tumor embolism into the pulmonary arteries and improved short-term survival.

[Indexed for MEDLINE]

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