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Paediatr Anaesth. 2004 Nov;14(11):960-3.

Liver biopsy complicated by hemorrhage in a patient with ARC syndrome.

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Department of Anesthesia, Hospital for Sick Children, University Avenue, Toronto, Ontario, Canada.


ARC syndrome is a rare disorder consisting of arthrogryposis, renal tubular acidosis and cholestatic liver disease. We report the case of a 5-week-old patient who underwent a percutaneous liver biopsy complicated by hemorrhage, and was subsequently diagnosed with ARC syndrome. A review of the literature demonstrates that these patients are at increased risk of bleeding caused by platelet dysfunction. The evaluation and management of unexpected hemorrhage in pediatric patients as a result of undiagnosed congenital bleeding problems is discussed.

[Indexed for MEDLINE]

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