Format

Send to

Choose Destination
Indian J Pathol Microbiol. 2003 Apr;46(2):217-9.

Combined occurrence of von Willebrand's disease and factor XIII deficiency: a case report.

Author information

1
Department of Hematology, All India Institute of Medical Sciences, New Delhi. vvbatraa@2rediffmail.com

Abstract

We report the case of a three year old female child with combined occurrence of von Willebrand's disease and factor XIII deficiency, an extremely rare combination. The patient presented with prolonged bleeding following cuts and wounds. Clot solubility test using 5M urea was positive. Platelet aggregation using ristocetin was reduced, which corrected on adding normal plasma. Aggregation with other agonists was normal. We discuss the clinico- hematological profile of the case. Only one such case has been reported in literature in the past to the best of our knowledge.

PMID:
15022915
[Indexed for MEDLINE]

Supplemental Content

Loading ...
Support Center