Rare inherited bleeding disorders secondary to coagulation factors in Jordan: a nine-year study

Acta Haematol. 1992;88(1):11-3. doi: 10.1159/000204587.

Abstract

This work reports on rare inherited coagulation factors defects which were seen in a developing country over a 9-year period. There were a total of 30 cases which fulfilled this diagnosis. Fibrinogen abnormalities were the most frequently encountered. There were 10 patients with afibrinogenemia, 2 with hypofibrinogenemia and 1 case with dysfibrinogenemia. Factor XI deficiency was found in 7 patients, factor V and VII deficiencies accounted for 3 cases each. Factor X and XIII deficiencies were found in 2 patients each. All these rare deficiencies accounted for 10% of all inherited bleeding disorders in the population studied over 9 years.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Blood Coagulation Disorders / diagnosis
  • Blood Coagulation Disorders / epidemiology*
  • Blood Coagulation Disorders / genetics
  • Blood Coagulation Factors / analysis*
  • Blood Coagulation Tests
  • Humans
  • Jordan / epidemiology
  • Prevalence

Substances

  • Blood Coagulation Factors