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Prog Cardiovasc Dis. 2002 Nov-Dec;45(3):225-34.

Pulmonary hypertension associated with connective tissue disease.

Author information

1
Pulmonary Hypertension Center, University of Colorado Health Sciences Center, Denver, CO, USA.

Abstract

Pulmonary arterial hypertension is a life threatening complication of several connective tissue diseases including scleroderma (both diffuse and limited scleroderma, or the CREST syndrome--calcinosis cutis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, and telangectasia), systemic lupus erythomatosis (SLE), mixed connective tissue disease (MCTD), and less commonly, rheumatoid arthritis (RA) and dermatomyositis/polymyositis. This report reviews the occurrence of this complication, potential etiologies, clinical presentation, and treatment options.

PMID:
12525998
DOI:
10.1053/pcad.2002.129975
[Indexed for MEDLINE]

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