Format

Send to

Choose Destination
See comment in PubMed Commons below
Korean J Intern Med. 2001 Sep;16(3):201-4.

Intrathoracic malignant peripheral nerve sheath tumor in von Recklinghausen's disease.

Author information

1
Department of Internal Medicine, Chonbuk National University, School of Medicine, 634-18 Keumam-dong, Duckjin-ku, Chonju 561-712, Chonbuk, South Korea.

Abstract

Malignant peripheral nerve sheath tumor (MPNST) is defined as any malignant tumor arising from or differentiating toward the cells of the peripheral nerve sheath. MPNST accounts for about 5-10% of all soft tissue tumors and is often associated with neurofibromatosis type I (NF-1, von Recklinghausen's disease). It is one of the malignant tumors associated with von Recklinghausen's disease. Its common site is the lower and upper extremities, trunk, head and neck. But intrathoracic manifestations are very rare. We report a case of a 40 year-old man with multiple neurofibromatosis who was presented with an intrathoracic malignant peripheral nerve sheath tumor.

PMID:
11769579
PMCID:
PMC4531729
[Indexed for MEDLINE]
Free PMC Article
PubMed Commons home

PubMed Commons

0 comments
How to join PubMed Commons

    Supplemental Content

    Full text links

    Icon for Publishing M2Community Icon for PubMed Central
    Loading ...
    Support Center